Double aortic arch and complex cardiac malformations.

Vascular ring caused by double aortic arch most commonly occurs as an isolated anomaly (Keith, Rowe, and Vlad, I967). However, its association with pulmonary stenosis (Bahnson and Blalock, I950), tetralogy of Fallot (Griswold and Young, I949; Stewart, Kincaid, and Edwards, I964), truncus arteriosus (Kerwin, I936), ventricular septal defect and left superior vena cava (Lincoln et al., I969), and coarctation (Stewart et al., I964), has been described. This paper reports the association of double aortic arch and D-transposition of the great arteries, ventricular septal defect, and pulmonary stenosis, and is thought to be the first such case report.